国際心臓血管研究ジャーナル

A Rare Case of a Giant Primary Cardiac Angiosarcoma Revealed by Superior Vena Cava Syndrome and Right Heart Failure

Zeine El Abasse*, Rime Benmalek, Nassour Brahim and Choukrani Hanane

Primary cardiac tumors are very rare with an incidence ranging from 0.0017% to 0.003% according to surgery and autopsy reports [1]. Among them, only 25% are malignant and nearly 75% are sarcoma and around 40% are angiosarcomas [2]. Sarcomas are often metastatic and have a poor prognosis even after surgical removal with an average mean survival of 6 months [3].