耳鼻科ジャーナル

Alveolar Soft Part Sarcoma Presenting with Nasal Obstruction

Neslihan Yaprak, Havva Serap Toru , Irem Hicran Ozbudak and Kenan Güney

Alveolar soft part sarcoma (ASPS) was first described by Christopherson et al. ASPS is a slow-growing and rare soft tissue tumor that usually occurs in young adults; patients are most often diagnosed between the ages of 15-35 years. ASPS are mainly located on the lower extremities, but can also be found on the arms, chest, and retroperitoneal areas. In children, ASPS are often found around the head and neck, especially on the tongue and orbita. ASPS is more common in women than in men, and the metastasis incidence ranges between 21% and 65% at the time of diagnosis. ASPS most commonly metastasize to the lungs, but also frequently metastasize to the bones and brain. In adults, ASPS is quite rare around head and neck. This study aimed to review the general approach to an adult patient with ASPS located in the nasal cavity.